Brown syndrome associated with Marcus-Gunn jaw winking ptosis
Keywords:Brown syndrome, superior oblique tendon, trochlea, Marcus-Gunn, jaw winking ptosis, blepharoptosis, aberrant innervation
Brown syndrome is a rare mechanical disorder characterized by restriction of the superior oblique trochlea-tendon complex. Marcus-Gunn jaw winking ptosis is a more common congenital oculofacial synkinesis in which blepharoptosis is associated with upper eyelid contraction that accompanies jaw movement. In this report, we present the case of a 50-year-old woman with unilateral Brown syndrome and Marcus-Gunn jaw winking ptosis in the fellow eye.
Wilson ME, Eustis HS Jr, Parks MM. Brown's syndrome. Surv Ophthalmol. 1989; 34(3): 153-72.
Gunn RM. Congenital ptosis with peculiar associated movements of the affected lid. Trans Ophthal Soc UK. 1883; 3: 283-7.
Disorders of the eyelids. In: Kanski JJ, ed. Clinical Ophthalmology, 3rd ed. Butterworth-Heinemann Medical; 1997, p. 1-26.
Torres MR, Calixto N Jr, Oliveira LR, et al. Marcus-Gunn Phenomenon: differential diagnosis of palpebral ptoses in children. J Pediatr (Rio J). 2004 May-Jun;80(3):249-52.
Sundareswaran S, Nipun CA, Kumar V. Jaw - winking phenomenon: Report of a case with review of literature. Indian J Dent Res. 2015; 26(3): 320-3.
Pratt SP, Beyer CK, Johnson CC. The Marcus-Gunn phenomenon. Ophthalmology. 1984; 91: 27-30.
Brodsky MC, Pollock SC, Buckley EG. Neural misdirection in congenital ocular fibrosis syndrome: implications and pathogenesis. J Pediatr Ophtalmol Strabismus. 1989; 26(4): 159-61.
Isenberg S, Blechman B. Marcus-Gunn jaw winking and Duane's retraction syndrome. J Pediatr Ophthalmol Strabismus. 1983; 20(6): 235-7.
Szretter K, Wójtowicz S. An atypical case of unilateral Brown's syndrome with coexisting abortive Marcus-Gunn synkinetic movements. Klin Oczna. 1968; 38(2): 405-9.
Artifoni E, Bertoncini G. On a rare familial association of the Brown syndrome with the Marcus-Gunn phenomenon. Ann Ottalmol Clin Ocul. 1965; 91(7): 563-76.
An Open Access Publication is one that meets the following two conditions:
1. The author(s) and copyright holder(s) grant(s) to all users a free, irrevocable, worldwide, perpetual right of access to, and a license to copy, use, distribute, transmit and display the work publicly and to make and distribute derivative works, in any digital medium for any responsible purpose, subject to proper attribution of authorship, as well as the right to make small numbers of printed copies for their personal use.
2. A complete version of the work and all supplemental materials, including a copy of the permission as stated above, in a suitable standard electronic format is deposited immediately upon initial publication in at least one online repository that is supported by an academic institution, scholarly society, government agency, or other well-established organization that seeks to enable open access, unrestricted distribution, interoperability, and long-term archiving.
Authors who publish with this journal agree to the following terms: 1. Authors retain copyright and grant the journal right of first publication with the work simultaneously licensed under a Creative Commons Attribution License that allows others to share the work with an acknowledgement of the work's authorship and initial publication in this journal. 2. Authors are able to enter into separate, additional contractual arrangements for the non-exclusive distribution of the journal's published version of the work (e.g., post it to an institutional repository or publish it in a book), with an acknowledgement of its initial publication in this journal. 3. Authors are permitted and encouraged to post their work online (e.g., in institutional repositories or on their website) prior to and during the submission process, as it can lead to productive exchanges, as well as earlier and greater citation of published work.